[Prognostic factors related to mortality of children with atresia of bile ducts]. Publisher: Introducción: la atresia de vías biliares (AVB) es el resultado final de un. Atresia de vías biliares vs. Hepatitis neonatal por citomegalovirus y toxoplasmosis, ¿patologías coexistentes o relación causa efecto?. Biliary Atresia – Clinical Series. Atresia das Vias Biliares – Revisão Casuística. Bárbara Netoa, Mariana Borges-Diasa, Eunice Trindadeb, José Estevão-Costaa, .

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Descriptive, observational, and retrospective study, including the patients with biliary atresia, diagnosed and treated between January 1, and December viae, SNIP measures contextual citation impact by wighting citations based on the total number of citations in a subject field. Como citar este artigo. Orphanet J Rare Dis ;1: Hepatology, 29pp.

Atresia das Vias Biliares: Revisão Casuística

Potential errors in the diagnosis and surgical management of neonatal jaundice. Gastrointest Endosc, 37pp. The presentation and evolution of patients was similar to other studies.

Acta Pediatr, 82pp. Age at surgery and recurrence of cholangitis were the only factors significantly related to prognosis.

Nonetheless, there was a statistically significant association between the development of multiple cholangitis episodes and the survival prognosis, which is in accordance to the literature [6, 7], where it is thought that the recurrence of this complication is an important prognostic factor when it comes to the evolution of this disease.


Prognosis of biliary atresia in the era of liver transplantation: Despite the average number of 1.

J Pediatr Surg, 32pp. Arch Dis Child ; There was a positive relation, with statistical significance, to native liver survival in patients who were submitted to surgery before 72 days of life, which supports the data referred re in other studies.

A year UNOS review of mortality and risk factors in young children awaiting liver transplantation. The most important factor associated with mortality in these patients is to perform KP.

[Prognostic factors related to mortality of children with atresia of bile ducts].

All the patients were viqs UDCA in the postoperative period, even though its beneficial effects, related to the increase in biliary acid drainage, hence preventing fibrosis and consequent progression of hepatic injury and a possible immunomodulator effect [4, 15], are still unclear [9, 12].

The efficacy of Kasai operation for biliary atresia: J Pediatr Gastroenterol Nutr, 4 attesia, pp. It was noticed that, during the period of this study, while hepatobiliary scintigraphy lost relevance, MRCP gained some importance as a diagnostic method.

It was noticed that those in whom surgery was performed before 72 days of age Extrahepatic biliary atresia is the main indication for liver transplantation among pediatric patients. In this study, a rate of However, a statistically significant difference was not documented when comparing preoperative levels to the prognosis of this disease.

The sample size is an atresis limitation to the statistical analysis of the collected data.

Curr Gastroenterol Rep ; Nutritional aspects of chronic liver disease and liver transplantation in children. Subscribe to our Newsletter. Life after portoenterostomy in biliary atresia. Soporte nutricional y tratamiento sustitutivo. All the contents of this journal, except where otherwise noted, is stresia under a Creative Commons Attribution License.


An evolution was noted when it comes to diagnostic tests, seeing that there was a progressive replacement of hepatobiliary scintigraphy by MRCP. The immune response, especially the predominant TH1 and interferon-gamma responses, genetic susceptibility and disorders related to the embryonic development of the biliary tree can play a role in the etiopathogenesis of extrahepatic biliary atresia.

In this clinical series, in J Pediatr Surg, 27pp. The future role of hepatic portoenterostomy as treatment of biliary atresia. Among those patients who had other associated malformations 5only one needed liver transplant. KPthe age at delivery was 4. J Pediatr Gastroenterol Nutr, 12pp. Out of the possible complications, the most common are cholangitis, portal hypertension, and cirrhosis [1]. Eur J Pediatr Surg, 8pp.

Si continua navegando, consideramos que acepta su uso. Yet today, portoenterostomy is the only available treatment, with better results when performed in the first 2 months of life. J Pediatr Gastroenterol Nutr, 30pp. Pediatr Ds North Am, 43pp. J Pediatr Surg, 21pp. At 6 weeks, 6 months, and annually after surgery, it was analyzed: